A child with severe inner ear malformations with favorable hearing utilization and balance functions after wearing hearing aids
Yusuke Kimura
Takeshi Masuda
Akifumi Tomizawa
Hideaki Sakata
Kimitaka Kaga
摘要：Infants with congenital deafness caused by severe bilateral inner ear malformations frequently suffer from severe hearing loss and poor balance. Unfortunately, the use of hearing aids is usually ineffective in recovering hearing, necessitating cochlear implants. We report a case of a 6-year-old boy with congenital deafness and bilateral inner ear malformations (right side, incomplete partition type I [IP-I];left side, common cavity deformity). Hearing aids had a remarkable effect in this patient, enabling sufficient and favorable hearing recovery such as to allow the patient to engage in daily conversations. Per-rotatory nystagmus was recorded on an electronystagmogram for both right and left rotations in a damped rotational chair test. It is rare for deaf children with severe bilateral inner ear malformation to demonstrate favorable development in hearing and good equilibrium function. Our findings suggest that auditory—vestibular hair cells in this patient may have been partially preserved despite IP-I in the right ear and common cavity deformity of the left ear. Copyright ? 2017, PLA General Hospital Department of Otolaryngology Head and Neck Surgery. Production and hosting by Elsevier (Singapore) Pte Ltd. This is an open access article under the CC BY-NC-ND license.
机标关键词：hearing aidsinner earcochlear implantshearing lossopen accesshair cells
论文发表日期：2017-01-01
在线出版日期：2025-08-15（本平台首次上网日期，不代表文献的发表时间）
页数：6( 41-46 )
英文信息