Intravenous leiomyomatosis presenting as pulmonary embol-ism:a cardiovascular perspective in two cases
Xia WU
Shi-Jie YANG
Ying LIANG
Emergency Critical Care Center,Beijing Anzhen Hospital,Capital Medical University,Beijing,China
摘要:Intravenous leiomyomatosis (IVL) is a rare,histolo-gically benign uterine smooth muscle tumor with malignant biological behavior due to its propensity for intravascular extension.[1]While gynecological in ori-gin,its most severe manifestations are cardiovascular,ari-sing from tumor propagation through the venous system into the inferior vena cava (IVC),right heart,and pulmon-ary arteries,mimicking thromboembolic disease.[2,3]This can lead to pulmonary embolism (PE),right heart obst-ruction,and even sudden cardiac death.[4]Diagnosis is ch-allenging,often delayed by misdiagnosis as conventional PE. We present two cases of IVL initially presenting with PE,highlighting the critical cardiovascular implications and diagnostic pitfalls.
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论文发表日期:2025-12-30
在线出版日期:2026-01-09(本平台首次上网日期,不代表文献的发表时间)
页数:3( 992-994 )
